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| Full Text | Issue Date | Title | Author(s) |  | 2011 | Cell biological consequences of Leigh disease. | Distelmaier, F.; Willems, P.H.; Smeitink, J.A.; Koopman, W.J.; Mayatepek, E. |
| | 2011 | Analyzing the homeostasis of T cell signaling proteins by a combination of Western Blot and Fluorescence Correlation Spectroscopy. | Chung, Y.D.; Sinzinger, M.D.S.; Bovee-Geurts, P.H.; Krause, M.; Dinkla, S.; Joosten, I.; Koopman, W.J.; Adjobo-Hermans, M.J.W.; Brock, R.E. |
 | 2011 | Solute diffusion is hindered in the mitochondrial matrix | Dieteren, C.E.J.; Gielen, S.C.A.M.; Nijtmans, L.G.J.; Smeitink, J.A.M.; Swarts, H.G.P.; Brock, R.; Willems, P.H.G.M.; Koopman, W.J.H. |
| | 2011 | Myotonic dystrophy (DM1) and dysphagia: the need for dysphagia management guidelines and an assessment tool | LaDonna, K.A.; Koopman, W.J.H.; Venance, S.L. |
| | 2011 | Depletion of PINK1 affects mitochondrial metabolism, calcium homeostasis and energy maintenance | Heeman, B.; Haute, C. Van den; Aelvoet, S.A.; Valsecchi, F.; Rodenburg, R.J.T.; Reumers, V.; Debyser, Z.; Callewaert, G.; Koopman, W.J.H.; Willems, P.H.G.M.; Baekelandt, V. |
| | 2011 | G37R SOD1 mutant alters mitochondrial complex I activity, Ca(2+) uptake and ATP production. | Coussee, E.; Smet, P. De; Bogaert, E.; Elens, I.; Damme, P. van; Willems, P.H.G.M.; Koopman, W.J.H.; Bosch, L.; Callewaert, G. |
| | 2011 | Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency | Koene, S.; Willems, P.H.G.M.; Roestenberg, P.M.H.; Koopman, W.J.H.; Smeitink, J.A.M. |
| | 2011 | Quantitative glucose and ATP sensing in mammalian cells | Liemburg-Apers, D.C.; Imamura, H.; Forkink, M.; Nooteboom, M.; Swarts, H.G.P.; Brock, R.E.; Smeitink, J.A.M.; Willems, P.H.G.M.; Koopman, W.J.H. |
| | 2011 | Isolated mitochondrial complex I deficiency: explorative data analysis of patient cell parameters. | Blanchet, L.M.; Buydens, M.C.; Smeitink, J.A.M.; Willems, P.H.G.M.; Koopman, W.J.H. |
| | 2011 | Restoration of complex V deficiency caused by a novel deletion in the human TMEM70 gene normalizes mitochondrial morphology | Jonckheere, A.I.; Huigsloot, M.; Lammens, M.M.Y.; Jansen, J.; Heuvel, L.P.W.J. van den; Spiekerkoetter, U.; Kleist-Retzow, J.C. von; Forkink, M.; Koopman, W.J.H.; Szklarczyk, R.J.; Huynen, M.A.; Fransen, J.; Smeitink, J.A.M.; Rodenburg, R.J.T. |
| | 2011 | Defective mitochondrial translation differently affects the live cell dynamics of complex I subunits | Dieteren, C.E.J.; Willems, P.H.G.M.; Swarts, H.G.P.; Fransen, J.; Smeitink, J.A.M.; Koopman, W.J.H.; Nijtmans, L.G.J. |
| | 2010 | Weak mitochondrial targeting sequence determines tissue-specific subcellular localization of glutamine synthetase in liver and brain cells. | Matthews, G.D.; Gur, N.; Koopman, W.J.H.; Pines, O.; Vardimon, L. |
| | 2010 | Complex I disorders: causes, mechanisms, and development of treatment strategies at the cellular level. | Valsecchi, F.; Koopman, W.J.H.; Manjeri, G.R.; Rodenburg, R.J.T.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2010 | Detection and manipulation of mitochondrial reactive oxygen species in mammalian cells. | Forkink, M.; Smeitink, J.A.M.; Brock, R.E.; Willems, P.H.G.M.; Koopman, W.J.H. |
 | 2010 | Mammalian mitochondrial complex I: biogenesis, regulation, and reactive oxygen species generation. | Koopman, W.J.H.; Nijtmans, L.G.J.; Dieteren, C.E.J.; Roestenberg, P.M.H.; Valsecchi, F.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2009 | The use of fluorescence correlation spectroscopy to probe mitochondrial mobility and intramatrix protein diffusion | Willems, P.H.G.M.; Swarts, H.G.P.; Hink, M.A.; Koopman, W.J.H. |
| | 2009 | C. elegans ATAD-3 is essential for mitochondrial activity and development. | Hoffmann, M.; Bellance, N.; Rossignol, R.; Koopman, W.J.H.; Willems, P.H.G.M.; Mayatepek, E.; Bossinger, O.; Distelmaier, F. |
| | 2009 | Calcium and ATP handling in human NADH:Ubiquinone oxidoreductase deficiency. | Valsecchi, F.; Esseling, J.J.; Koopman, W.J.H.; Willems, P.H.G.M. |
| | 2009 | Tracing human mitochondrial complex I assembly by use of GFP-tagged subunits | Dieteren, C.E.J.; Koopman, W.J.H.; Nijtmans, L.G.J. |
| | 2009 | The antioxidant Trolox restores mitochondrial membrane potential and Ca2+ -stimulated ATP production in human complex I deficiency. | Distelmaier, F.; Visch, H.J.; Smeitink, J.A.M.; Mayatepek, E.; Koopman, W.J.H.; Willems, P.H.G.M. |
| | 2009 | Mitochondrial complex I deficiency: from organelle dysfunction to clinical disease. | Distelmaier, F.; Koopman, W.J.H.; Heuvel, L.P.W.J. van den; Rodenburg, R.J.T.; Mayatepek, E.; Willems, P.H.G.M.; Smeitink, J.A.M. |
| | 2009 | Mitochondrial dynamics in human NADH:ubiquinone oxidoreductase deficiency. | Willems, P.H.G.M.; Smeitink, J.A.M.; Koopman, W.J.H. |
| | 2008 | Mitochondrial Ca2+ homeostasis in human NADH:ubiquinone oxidoreductase deficiency. | Willems, P.H.G.M.; Valsecchi, F.; Distelmaier, F.; Verkaart, S.; Visch, H.J.; Smeitink, J.A.M.; Koopman, W.J.H. |
| | 2008 | Computer-assisted live cell analysis of mitochondrial membrane potential, morphology and calcium handling. | Koopman, W.J.H.; Distelmaier, F.; Esseling, J.J.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2008 | Subunits of mitochondrial complex I exist as part of matrix- and membrane-associated subcomplexes in living cells. | Dieteren, C.E.J.; Willems, P.H.G.M.; Vogel, R.O.; Swarts, H.G.P.; Fransen, J.; Roepman, R.; Crienen, G.; Smeitink, J.A.M.; Nijtmans, L.G.J.; Koopman, W.J.H. |
| | 2008 | Mitochondrial processes are impaired in hereditary inclusion body myopathy. | Eisenberg, I.; Novershtern, N.; Itzhaki, Z.; Becker-Cohen, M.; Sadeh, M.; Willems, P.H.G.M.; Friedman, N.; Koopman, W.J.H.; Mitrani-Rosenbaum, S. |
| | 2008 | Mitochondrial function and morphology are impaired in parkin-mutant fibroblasts. | Mortiboys, H.; Thomas, K.J.; Koopman, W.J.H.; Klaffke, S.; Abou-Sleiman, P.; Olpin, S.; Wood, N.W.; Willems, P.H.G.M.; Smeitink, J.A.M.; Cookson, M.R.; Bandmann, O. |
| | 2008 | Inherited complex I deficiency is associated with faster protein diffusion in the matrix of moving mitochondria | Koopman, W.J.H.; Distelmaier, F.; Hink, M.A.; Verkaart, S.; Wijers, M.; Fransen, J.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2008 | Mitigation of NADH: ubiquinone oxidoreductase deficiency by chronic Trolox treatment. | Koopman, W.J.H.; Verkaart, S.; Emst-de Vries, S.E. van; Grefte, S.; Smeitink, J.A.M.; Nijtmans, L.G.J.; Willems, P.H.G.M. |
| | 2007 | Hydrogenosomes (and related organelles, either) are not the same | Hackstein, J.H.P.; Tjaden, J.; Koopman, W.J.H.; Huijnen, M.A.; Martin, William F.; Müller, Miklós |
| | 2007 | Insights into the genome of large sulfur bacteria revealed by analysis of single filaments. | Mussmann, M.; Hu, F.Z.; Richter, M.; Beer, D. de; Preisler, A.; Jorgensen, B.B.; Huntemann, M.; Glockner, F.O.; Amann, R.; Koopman, W.J.H.; Lasken, R.S.; Janto, B.; Hogg, J.; Stoodley, P.; Boissy, R.; Ehrlich, G.D. |
| | 2007 | Phytanic acid impairs mitochondrial respiration through protonophoric action. | Komen, J.C.; Distelmaier, F.; Koopman, W.J.H.; Wanders, R.J.A.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2007 | Partial complex I inhibition decreases mitochondrial motility and increases matrix protein diffusion as revealed by fluorescence correlation spectroscopy. | Koopman, W.J.H.; Hink, M.A.; Verkaart, S.A.J.; Visch, H.J.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2007 | Human NADH : ubiquinone oxidoreductase deficiency : radical changes in mitochondrial morphology? | Koopman, W.J.H.; Verkaart, S.A.J.; Visch, H.J.; Vries, S. de; Nijtmans, L.G.J.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2007 | Cytosolic signaling protein Ecsit also localizes to mitochondria where it interacts with chaperone NDUFAF1 and functions in complex I assembly. | Vogel, R.O.; Janssen, R.J.R.J.; Brand, M.A.M. van den; Dieteren, C.E.J.; Verkaart, S.A.J.; Koopman, W.J.H.; Willems, P.H.G.M.; Pluk, W.; Heuvel, L.P.W.J. van den; Smeitink, J.A.M.; Nijtmans, L.G.J. |
| | 2007 | Superoxide production is inversely related to complex I activity in inherited complex I deficiency. | Verkaart, S.A.J.; Koopman, W.J.H.; Emst-de Vries, S.E. van; Nijtmans, L.G.J.; Heuvel, L.W. van den; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2007 | Identification of mitochondrial complex I assembly intermediates by tracing tagged NDUFS3 demonstrates the entry point of mitochondrial subunits. | Vogel, R.O.; Dieteren, C.E.J.; Heuvel, L.P.W.J. van den; Willems, P.H.G.M.; Smeitink, J.A.M.; Koopman, W.J.H.; Nijtmans, L.G.J. |
| | 2007 | Mitochondrial and cytosolic thiol redox state are not detectably altered in isolated human NADH:ubiquinone oxidoreductase deficiency. | Verkaart, S.A.J.; Koopman, W.J.H.; Cheek, J.; Emst-de Vries, S.E. van; Heuvel, L.W. van den; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2006 | Simultaneous quantification of oxidative stress and cell spreading using 5-(and-6)-chloromethyl-2',7'-dichlorofluorescein. | Koopman, W.J.H.; Verkaart, S.A.J.; Emst-de Vries, S.E. van; Grefte, S.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2006 | Simultaneous quantitative measurement and automated analysis of mitochondrial morphology, mass, potential, and motility in living human skin fibroblasts. | Koopman, W.J.H.; Visch, H.J.; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2006 | Decreased agonist-stimulated mitochondrial ATP production caused by a pathological reduction in endoplasmic reticulum calcium content in human complex I deficiency. | Visch, H.J.; Koopman, W.J.H.; Leusink, A.; Emst-de Vries, S.E. van; Heuvel, L.W. van den; Willems, P.H.G.M.; Smeitink, J.A.M. |
| | 2006 | Ca2+-mobilizing agonists increase mitochondrial ATP production to accelerate cytosolic Ca2+ removal : aberrations in human complex I deficiency | Visch, H.J.; Koopman, W.J.H.; Zeegers, D.; Emst-de Vries, S.E. van; Kuppeveld, F.J.M. van; Heuvel, L.W. van den; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2005 | Amplitude modulation of nuclear Ca 2+ signals in human skeletal myotubes: A possible role for nuclear Ca 2+ buffering | Koopman, W.J.H.; Willems, P.H.G.M.; Oosterhof, A.; Kuppevelt, A.H.M.S.M. van; Gielen, S.C.A.M. |
| | 2005 | An anaerobic mitochondrion that produces hydrogen | Boxma, B.; Graaf, R.M. de; Staay, G.W.M. van der; Alen, T.A. van; Ricard, G.; Gabaldon, T.; Hoek, A.H.A.M. van; Moon-van der Staay, S.Y.; Koopman, W.J.H.; Hellemond, J.J. van; Tielens, A.G.; Friedrich, T.; Veenhuis, M.; Huynen, M.A.; Hackstein, J.H.P. |
| | 2005 | Decreased agonist-stimulated mitochondrial ATP production caused by a pathological reduction in endoplasmic reticulum calcium content in human complex I deficiency. | Visch, H.J.; Koopman, W.J.H.; Leusink, A.; Emst-de Vries, S.E. van; Heuvel, L.W. van den; Willems, P.H.G.M.; Smeitink, J.A.M. |
| | 2005 | Mitochondrial network complexity and pathological decrease in complex I activity are tightly correlated in isolated human complex I deficiency | Koopman, W.J.H.; Visch, H.J.; Verkaart, S.A.J.; Heuvel, L.W. van den; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2005 | Inhibition of complex I of the electron transport chain causes O2-. -mediated mitochondrial outgrowth | Koopman, W.J.H.; Verkaart, S.A.J.; Visch, H.J.; Westhuizen, F.H. van der; Murphy, M.; Heuvel, L.W. van den; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2004 | Cell Biological Consequences of Mitochondrial NADH : Ubiquinone Oxidoreductase Deficiency | Smeitink, J.A.M.; Heuvel, L.P.W.J. van den; Koopman, W.J.H.; Nijtmans, L.G.J.; Ugalde, C.; Willems, P.H.G.M. |
| | 2004 | Inhibition of mitochondrial Na+-Ca2+ exchange restores agonist-induced ATP production and Ca2+ handling in human complex I deficiency. | Visch, H.J.; Rutter, G.A.; Koopman, W.J.H.; Koenderink, J.B.; Verkaart, S.A.J.; Groot, T. de; Varadi, A.; Mitchell, K.J.; Heuvel, L.P.W.J. van den; Smeitink, J.A.M.; Willems, P.H.G.M. |
| | 2000 | The Syntax of early English | Fischer, O.; Kemenade, A.M.C. van; Koopman, W.J.H.; Wurff, W. van der |
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